Características clínicas do paciente com mucopolissacaridose tipo IIA e suas implicações para o tratamento odontológico : relato de caso

Abstract

Mucopolysaccharidosis (MPS) is a disease described by the innate error in the metabolism of glycosaminoglycans (GAGs). MPS II or Hunter's Syndrome is caused by deficiency of the iduronate-2-sulfatase (I2S) enzyme and is the most common form of MPS. Characterized by involvement of nervous, cardiovascular, respiratory and mucoskeletal systems, along with numerous oral manifestations. The objective of this study is to describe the clinical characteristics of MPS and present the case of a patient with Hunter syndrome. Patient M.A.O.S, male, 15 years old, attended the clinic of Patients with Special Needs of the Dental Polyclinic of the State University of Amazonas, where anamnesis, clinical examination and subsequent dental treatment necessary for the clinical condition presented by the patient were performed. We highlight the importance of dentists in the diagnosis and planning of the treatment of patients diagnosed with such systemic conditions and we realize the importance of integrating the multidisciplinary team aiming at improving the quality of life